By Scientia Professor Matthew Colm Kiernan

Journal articles

Ahmed RM; Devenney EM; Strikwerda-Brown C; Hodges JR; Piguet O; Kiernan MC, 2020, 'Phenotypic variability in ALS-FTD and effect on survival', Neurology, 94, pp. E2005 - E2013, http://dx.doi.org/10.1212/WNL.0000000000009398

Menon P; Higashihara M; van den Bos M; Geevasinga N; Kiernan MC; Vucic S, 2020, 'Cortical hyperexcitability evolves with disease progression in ALS', Annals of Clinical and Translational Neurology, 7, pp. 733 - 741, http://dx.doi.org/10.1002/acn3.51039

Higashihara M; Van den Bos MAJ; Menon P; Kiernan MC; Vucic S, 2020, 'Interneuronal networks mediate cortical inhibition and facilitation', Clinical Neurophysiology, 131, pp. 1000 - 1010, http://dx.doi.org/10.1016/j.clinph.2020.02.012

Kiernan MC, 2020, 'Queen Square: a history of the National Hospital and its Institute of Neurology', JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 91, pp. 560 - 561, http://dx.doi.org/10.1136/jnnp-2020-322776

Vucic S; Higashihara M; Sobue G; Atsuta N; Doi Y; Kuwabara S; Kim SH; Kim I; Oh KW; Park J; Kim EM; Talman P; Menon P; Kiernan MC, 2020, 'ALS is a multistep process in South Korean, Japanese, and Australian patients', Neurology, 94, pp. E1657 - E1663, http://dx.doi.org/10.1212/WNL.0000000000009015

Weiss M; Macklin E; McIlduff C; Vucic OS; Wainger B; Kiernan M; Goutman S; Goyal N; Rutkove S; Ladha S; Chen A; Harms M; Brannagan T; Lacomis D; Zivkovic S; Ma M; Wang L; Simmons Z; Rivner M; Shefner J; Cudkowicz M; Atassi N, 2020, 'Effects of Mexiletine on Cortical and Peripheral Nerve Hyperexcitability in Sporadic ALS (2531)', Neurology, 94, http://dx.doi.org/10.1212/wnl.94.15_supplement.2531

Kandula T; Farrar MA; Cohn RJ; Carey KA; Johnston K; Kiernan MC; Krishnan AV; Park SB, 2020, 'Changes in long term peripheral nerve biophysical properties in childhood cancer survivors following neurotoxic chemotherapy', Clinical Neurophysiology, 131, pp. 783 - 790, http://dx.doi.org/10.1016/j.clinph.2019.12.411

Dharmadasa T; Matamala JM; Howells J; Vucic S; Kiernan MC, 2020, 'Early focality and spread of cortical dysfunction in amyotrophic lateral sclerosis: A regional study across the motor cortices', Clinical Neurophysiology, 131, pp. 958 - 966, http://dx.doi.org/10.1016/j.clinph.2019.11.057

Turner MR; Barohn RJ; Corcia P; Fink JK; Harms MB; Kiernan MC; Ravits J; Silani V; Simmons Z; Statland J; Van Den Berg LH; Mitsumoto H, 2020, 'Primary lateral sclerosis: Consensus diagnostic criteria', Journal of Neurology Neurosurgery and Psychiatry, 91, pp. 373 - 377, http://dx.doi.org/10.1136/jnnp-2019-322541

Huynh W; Sharplin LE; Caga J; Highton-Williamson E; Kiernan MC, 2020, 'Respiratory function and cognitive profile in amyotrophic lateral sclerosis', European Journal of Neurology, 27, pp. 685 - 691, http://dx.doi.org/10.1111/ene.14130

Wan HWY; Carey KA; D'Silva A; Vucic S; Kiernan MC; Kasparian NA; Farrar MA, 2020, 'Health, wellbeing and lived experiences of adults with SMA: A scoping systematic review', Orphanet Journal of Rare Diseases, 15, pp. 70, http://dx.doi.org/10.1186/s13023-020-1339-3

Huynh W; Ahmed R; Mahoney CJ; Nguyen C; Tu S; Caga J; Loh P; Lin CSY; Kiernan MC, 2020, 'The impact of cognitive and behavioral impairment in amyotrophic lateral sclerosis', Expert Review of Neurotherapeutics, 20, pp. 281 - 293, http://dx.doi.org/10.1080/14737175.2020.1727740

Mahoney CJ; Kiernan MC, 2020, 'Expanding the availability of medications for amyotrophic lateral sclerosis in Australia', Medical Journal of Australia, 212, pp. 189 - 189.e1, http://dx.doi.org/10.5694/mja2.50482

Swash M; Burke D; Turner MR; Grosskreutz J; Leigh PN; Decarvalho M; Kiernan MC, 2020, 'Occasional essay: Upper motor neuron syndrome in amyotrophic lateral sclerosis', Journal of Neurology Neurosurgery and Psychiatry, 91, pp. 227 - 234, http://dx.doi.org/10.1136/jnnp-2019-321938

Tatkiewicz W; Dickie J; Bedford F; Jones A; Atkin M; Kiernan M; Maze EA; Agit B; Farnham G; Kanapin A; Belshaw R, 2020, 'Characterising a human endogenous retrovirus(HERV)-derived tumour-associated antigen: enriched RNA-Seq analysis of HERV-K(HML-2) in mantle cell lymphoma cell lines', MOBILE DNA, 11, http://dx.doi.org/10.1186/s13100-020-0204-1

Yeh WZ; Dyck PJ; Van Den Berg LH; Kiernan MC; Taylor BV, 2020, 'Multifocal motor neuropathy: controversies and priorities', Journal of Neurology Neurosurgery and Psychiatry, 91, pp. 140 - 148, http://dx.doi.org/10.1136/jnnp-2019-321532

Vucic S; Ryder J; Mekhael L; Henderson RD; Mathers S; Needham M; Schultz DW; Kiernan MC, 2020, 'Phase 2 randomized placebo controlled double blind study to assess the efficacy and safety of tecfidera in patients with amyotrophic lateral sclerosis (TEALS Study) Study protocol clinical trial (SPIRIT Compliant)', MEDICINE, 99, http://dx.doi.org/10.1097/MD.0000000000018904

Borire AA; Issar T; Kwai NC; Visser LH; Simon NG; Poynten AM; Kiernan MC; Krishnan AV, 2020, 'Sonographic assessment of nerve blood flow in diabetic neuropathy', Diabetic Medicine, 37, pp. 343 - 349, http://dx.doi.org/10.1111/dme.14085

Carter A; Richards LJ; Apthorp D; Azghadi MR; Badcock DR; Balleine B; Bekkers JM; Berk M; Bourne JA; Bradley AP; Breakspear M; Brichta A; Carter O; Castles A; Chakli K; Cohen-Woods S; Conn SJ; Cornish J; Cornish K; de Zubicaray G; Egan GF; Enticott PG; Fitzgibbon BM; Forlini C; Fornito A; Griffiths L; Gullifer J; Hall W; Halliday G; Hannan AJ; Harrer S; Harvey A; Hatherly C; Hickie IB; Kennett J; Kiernan M; Kilpatrick T; Kiral-Kornek I; Korgaonkar MS; Lawrence AJ; Leventer R; Levy N; Licinio J; Lovell N; Mackellar G; Malcolm L; Mason A; Mattingley JB; Medland SE; Michie PT; Nithianantharajah J; Parker J; Payne JM; Poole-Warren L; Sah P; Sarnyai Z; Schofield PR; Shimoni O; Shum DHK; Silk T; Slee M; Smith AE; Soulis T; Sriram S; Stuart GJ; Tapson J; Thompson MB; van Schaik A; Vincent NA; Vissel B; Waters A, 2020, 'Erratum: A Neuroethics Framework for the Australian Brain Initiative (Neuron (2019) 101(3) (365–369), (S0896627319300054), (10.1016/j.neuron.2019.01.004))', Neuron, 105, pp. 201, http://dx.doi.org/10.1016/j.neuron.2019.12.019

Tazelaar GHP; Boeynaems S; De Decker M; van Vugt JJFA; Kool L; Goedee HS; McLaughlin RL; Sproviero W; Iacoangeli A; Moisse M; Jacquemyn M; Daelemans D; Dekker AM; van der Spek RA; Westeneng HJ; Kenna KP; Assialioui A; Silva ND; Povedano M; Mora Pardina JS; Hardiman O; Salachas F; Millecamps S; Vourc’h P; Corcia P; Couratier P; Morrison KE; Shaw PJ; Shaw CE; Pasterkamp RJ; Landers JE; Van Den Bosch L; Robberecht W; Al-Chalabi A; van den Berg LH; Van Damme P; Veldink JH; van Es MA; Akçimen F; Al Khleifat A; Andersen P; Basak AN; Bauer DC; Blair I; Brands WJ; Byrne RP; Calvo A; Gonzalez YC; Chio A; Cooper-Knock J; de Carvalho M; Drory VE; Eitan C; Redondo AG; Gellera C; Glass JD; Gotkine M; Hornstein E; Kenna B; Kiernan MC; Kocoglu C; Kooyman M; Alonso VL; Middelkoop B; Mill J; Mitne-Neto M; Pinto S; Gromicho M; Panadés MP; Pulit SL; Ratti A; Schellevis RD; Shatunov A; Silani V; Staiger C; Ticozzi N; Tunca C; Twine NA; van Doormaal PTC; van Eijk KR; van Rheenen W; Visscher PM; Weber M; Williams KL; Wray N; Yang J; Zatz M; Zhang K, 2020, 'ATXN1 repeat expansions confer risk for amyotrophic lateral sclerosis and contribute to TDP-43 mislocalization', Brain Communications, 2, http://dx.doi.org/10.1093/braincomms/fcaa064

Kiernan MC, 2020, 'Jewels in the crown: A century of achievement for the Journal of Neurology, Neurosurgery & Psychiatry', Journal of Neurology Neurosurgery and Psychiatry, 91, http://dx.doi.org/10.1136/jnnp-2019-322443

Gulati G; Kiernan M; Sabe MA, 2020, 'Massive retroperitoneal hemorrhage after external shock wave lithotripsy in a patient with a left ventricular assist device', UROLOGY CASE REPORTS, 28, http://dx.doi.org/10.1016/j.eucr.2019.101033

Kiernan MC; Bostock H; Park SB; Kaji R; Krarup C; Krishnan AV; Kuwabara S; Lin CSY; Misawa S; Moldovan M; Sung J; Vucic S; Wainger BJ; Waxman S; Burke D, 2020, 'Measurement of axonal excitability: Consensus guidelines', Clinical Neurophysiology, 131, pp. 308 - 323, http://dx.doi.org/10.1016/j.clinph.2019.07.023

de Carvalho M; Kiernan MC; Pullman SL; Rezania K; Turner MR; Simmons Z, 2020, 'Neurophysiological features of primary lateral sclerosis', Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, 21, pp. 11 - 17, http://dx.doi.org/10.1080/21678421.2020.1837174

Mitsumoto H; Turner MR; Ajroud-Driss S; Andres P; Andrews J; Gomez EA; Atehortua JMS; Babu S; Barohn R; Bede P; Benatar M; Chew S; Conwit R; Corcia P; Cudkowicz M; Davis F; Carvalho MD; Drory V; Elman L; Factor-Litvak P; Fernandes JAM; Ferrey D; Finegan E; Fink J; Floeter MK; Fournier C; Genge A; Govindarajan R; Granit V; Haase G; Hardiman O; Harms M; Hayat G; Heiman-Patterson T; Hill B; Hübers A; Huey E; Jawdat O; Kano O; Kau K; Kiernan M; Kisanuki Y; Kurent J; Kwan J; Lange D; Ludolph A; Mackenzie I; Manfredi G; Marren D; Morita M; Murphy J; Nations S; Oskarsson B; Paganoni S; Pellerin D; Ravits J; Rezania K; Rouleau G; Scelsa S; Siddique T; Siddique N; Silani V; Simmons Z; Statland J; Traynor B; Blitterswijk MV; Berg LVD; Walk D; Warden D; Wymer J, 2020, 'Preface: promoting research in PLS: current knowledge and future challenges', Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, 21, pp. 1 - 2, http://dx.doi.org/10.1080/21678421.2020.1840795

Timmins HC; Li T; Kiernan MC; Horvath LG; Goldstein D; Park SB, 2020, 'Quantification of Small Fiber Neuropathy in Chemotherapy-Treated Patients', Journal of Pain, 21, pp. 44 - 58, http://dx.doi.org/10.1016/j.jpain.2019.06.011

Mahoney CJ; Highton-Williamson E; Howells J; Ahmed R; Huynh W; Kiernan MC, 2020, '11. Neurophysiological correlates of impaired cognition in Amyotrophic Lateral Sclerosis', Clinical Neurophysiology, 131, pp. e5 - e5, http://dx.doi.org/10.1016/j.clinph.2019.11.044

Silsby M; Fois AF; Yiannikas C; Kiernan MC; Fung VSC; Vucic S, 2020, '12. EMG bursting characteristics of upper limb muscles in patients with CIDP and tremor', Clinical Neurophysiology, 131, pp. e5 - e6, http://dx.doi.org/10.1016/j.clinph.2019.11.045

van den Bos MAJ; Higashihara M; Howells J; Parvathi Menon ; Geevasinga N; Kiernan MC; Vucic S, 2020, '13. Transcallosal dysfunction an early marker of ALS', Clinical Neurophysiology, 131, pp. e6 - e6, http://dx.doi.org/10.1016/j.clinph.2019.11.046

Nathani D; Spies J; Barnett M; Wang M-X; Pollard J; Kiernan M, 2020, '15. Paraproteinaemic neuropathy: The role for nerve biopsy', Clinical Neurophysiology, 131, pp. e7 - e7, http://dx.doi.org/10.1016/j.clinph.2019.11.048

Li T; Timmins HC; McCrary JM; Trinh T; Horvath LG; Friedlander ML; Kiernan MC; Goldstein D; Park SB, 2020, '5. Neurophysiological characteristics in the development and recovery of peripheral neuropathy in oxaliplatin and paxlitaxel treated patients', Clinical Neurophysiology, 131, pp. e2 - e3, http://dx.doi.org/10.1016/j.clinph.2019.11.038

Higashihara M; Menon P; Geevasinga N; Van den Bos MAJ; Kiernan MC; Vucic S, 2020, '6. Motor neuron disease with malignancy: a pathophysiologically distinct entity of motor neuron disease?', Clinical Neurophysiology, 131, pp. e3 - e3, http://dx.doi.org/10.1016/j.clinph.2019.11.039

Timmins HC; Li T; Huynh W; Kiernan MC; Baron-Hay S; Marx G; Boyle F; Goldstein D; Park SB, 2020, '8. Electrophysiological and phenotypic profiles of taxane-induced neuropathy', Clinical Neurophysiology, 131, pp. e4 - e4, http://dx.doi.org/10.1016/j.clinph.2019.11.041

Schijven D; Stevelink R; McCormack M; van Rheenen W; Luykx JJ; Koeleman BPC; Veldink JH, 2020, 'Analysis of shared common genetic risk between amyotrophic lateral sclerosis and epilepsy', NEUROBIOLOGY OF AGING, 92

McCann EP; Fifita JA; Grima N; Galper J; Mehta P; Freckleton SE; Zhang KY; Henden L; Hogan AL; Fat SCM; Wu SSL; Jagaraj CJ; Berning BA; Williams KL; Twine NA; Bauer D; Piguet O; Hodges J; Kwok JBJ; Halliday GM; Kiernan MC; Atkin J; Rowe DB; Nicholson GA; Walker AK; Blair IP; Yang S, 2019, 'Genetic and immunopathological analysis of CHCHD10 in Australian amyotrophic lateral sclerosis and frontotemporal dementia and transgenic TDP-43 mice', Journal of Neurology Neurosurgery and Psychiatry, 91, pp. 162 - 171, http://dx.doi.org/10.1136/jnnp-2019-321790

Yang Y; Halliday GM; Kiernan MC; Tan RH, 2019, 'TDP-43 levels in the brain tissue of ALS cases with and without C9ORF72 or ATXN2 gene expansions', Neurology, 93, pp. e1748 - e1755, http://dx.doi.org/10.1212/WNL.0000000000008439

Ahmed RM; Devenney EM; Strikwerda-Brown C; Hodges JR; Piguet O; Kiernan MC, 2019, 'COG-01 Phenotypic variation in 
ALS-FTD and effect on survival', Amyotrophic Lateral Sclerosis Frontotemporal Degeneration, 20, pp. 301 - 308, http://dx.doi.org/10.1080/21678421.2019.1647000

Kiernan MC, 2019, 'Milestones', Journal of Neurology Neurosurgery and Psychiatry, 90, pp. 1189, http://dx.doi.org/10.1136/jnnp-2019-321711

Cutler C; Kiernan M; Willis JR; Gallardo-Alfaro L; Casas-Agustench P; White D; Hickson M; Gabaldon T; Bescos R, 2019, 'Post-exercise hypotension and skeletal muscle oxygenation is regulated by nitrate-reducing activity of oral bacteria', FREE RADICAL BIOLOGY AND MEDICINE, 143, pp. 252 - 259, http://dx.doi.org/10.1016/j.freeradbiomed.2019.07.035

Issar T; Arnold R; Kwai NCG; Walker S; Yan A; Borire AA; Poynten AM; Pussell BA; Endre ZH; Kiernan MC; Krishnan AV, 2019, 'Relative contributions of diabetes and chronic kidney disease to neuropathy development in diabetic nephropathy patients', Clinical Neurophysiology, 130, pp. 2088 - 2095, http://dx.doi.org/10.1016/j.clinph.2019.08.005

Ahmed R; Devenney E; Hodges J; Piguet O; Kiernan M, 2019, 'Effect of phenotypic presentation on survival in ALS-FTD', JOURNAL OF THE NEUROLOGICAL SCIENCES, 405, http://dx.doi.org/10.1016/j.jns.2019.10.323

Ahmed R; Landin-Romero R; Liang C; Keogh J; Henning E; Emma D; Hodges J; Kiernan M; Sadaf F; Piguet O, 2019, 'Neural correlates of body composition in frontotemporal dementia', JOURNAL OF THE NEUROLOGICAL SCIENCES, 405, http://dx.doi.org/10.1016/j.jns.2019.10.840

Vucic S; Westeneng HJ; Al-Chalabi A; Van Den Berg LH; Talman P; Kiernan MC, 2019, 'Amyotrophic lateral sclerosis as a multi-step process: an Australia population study', Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, 20, pp. 532 - 537, http://dx.doi.org/10.1080/21678421.2018.1556697

Gold J; Rowe DB; Kiernan MC; Vucic S; Mathers S; van Eijk RPA; Nath A; Garcia Montojo M; Norato G; Santamaria UA; Rogers ML; Malaspina A; Lombardi V; Mehta PR; Westeneng HJ; van den Berg LH; Al-Chalabi A, 2019, 'Safety and tolerability of Triumeq in amyotrophic lateral sclerosis: the Lighthouse trial', Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, 20, pp. 595 - 604, http://dx.doi.org/10.1080/21678421.2019.1632899

Li T; Timmins H; King T; Kiernan M; Goldstein D; Park S, 2019, 'Bortezomib Induced Peripheral Neuropathy: A Systematic Review of Phase III Trials', CLINICAL LYMPHOMA MYELOMA & LEUKEMIA, 19, pp. E346 - E346, http://dx.doi.org/10.1016/j.clml.2019.09.571

Besomi M; Hodges PW; Van Dieën J; Carson RG; Clancy EA; Disselhorst-Klug C; Holobar A; Hug F; Kiernan MC; Lowery M; McGill K; Merletti R; Perreault E; Søgaard K; Tucker K; Besier T; Enoka R; Falla D; Farina D; Gandevia S; Rothwell JC; Vicenzino B; Wrigley T, 2019, 'Consensus for experimental design in electromyography (CEDE) project: Electrode selection matrix', Journal of Electromyography and Kinesiology, 48, pp. 128 - 144, http://dx.doi.org/10.1016/j.jelekin.2019.07.008

Ke YD; Chan G; Stefanoska K; Au C; Bi M; Müller J; Przybyla M; Feiten A; Prikas E; Halliday GM; Piguet O; Kiernan MC; Kassiou M; Hodges JR; Loy CT; Mattick JS; Ittner A; Kril JJ; Sutherland GT; Ittner LM, 2019, 'CNS cell type-specific gene profiling of P301S tau transgenic mice identifies genes dysregulated by progressive tau accumulation', Journal of Biological Chemistry, 294, pp. 14149 - 14162, http://dx.doi.org/10.1074/jbc.RA118.005263

Kiernan MC; Ziemann U; Eisen A, 2019, 'Amyotrophic lateral sclerosis: Origins traced to impaired balance between neural excitation and inhibition in the neonatal period', Muscle and Nerve, 60, pp. 232 - 235, http://dx.doi.org/10.1002/mus.26617

McMackin R; Muthuraman M; Groppa S; Babiloni C; Taylor JP; Kiernan MC; Nasseroleslami B; Hardiman O, 2019, 'Measuring network disruption in neurodegenerative diseases: New approaches using signal analysis', Journal of Neurology Neurosurgery and Psychiatry, 90, pp. 1011 - 1020, http://dx.doi.org/10.1136/jnnp-2018-319581

Higashihara M; Menon P; Geevasinga N; Van den Bos MAJ; Kiernan MC; Vucic S, 2019, 'Motor neuron disease with malignancy: Clinical and pathophysiological insights', Clinical Neurophysiology, 130, pp. 1557 - 1561, http://dx.doi.org/10.1016/j.clinph.2019.05.026

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